Segmental Neurofibromatosis Type 1, a Rare Variant of Neurofibromatosis: Report of Two Cases

Authors

  • Bagherani Nooshin
  • Yaghoobi Reza
Abstract:

Segmental neurofibromatosis type I (SNF-I) is a rare variant of neurofibromatosis (NF). It is classified as NF type V and defined as cafe'-au-lait macules and/or neurofibromas in a single ,unilateral segment of the body .We report two cases with SNF-I with striking similar manifestations.

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Journal title

volume 12  issue 1

pages  22- 25

publication date 2009-04-01

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